Craniofacial Fibrous Dysplasia: A Rare Disease

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Authors

  • Chaitanya Bharadwaj
     Associate Professor, Department of Otorhinolaryngology, Dr. Vasantrao Pawar Medical College, Hospital and Research Centre, Adgaon Nashik, Nashik – 422003 ,IN
  • Rushika Patel
     Assistant Professor, Department of Otorhinolaryngology, Dr. Vasantrao Pawar Medical College, Hospital and Research Centre, Adgaon Nashik, Nashik – 422003 ,IN
  • Shreeya Kulkarni
     Professor, Department of Otorhinolaryngology, Dr. Vasantrao Pawar Medical College, Hospital and Research Centre, Adgaon Nashik, Nashik – 422003 ,IN
  • Kiran Burse
     Professor and Head, Department of Otorhinolaryngology, Dr. Vasantrao Pawar Medical College, Hospital and Research Centre, Adgaon Nashik, Nashik – 422003 ,IN
  • Vandana Sancheti
     Senior Resident, Department of Otorhinolaryngology, Dr. Vasantrao Pawar Medical College, Hospital and Research Centre, Adgaon Nashik, Nashik – 422003 ,IN
  • Preeti Dudhe
     Former PG Resident, Department of Otorhinolaryngology, Dr. Vasantrao Pawar Medical College, Hospital and Research Centre, Adgaon Nashik, Nashik – 422003 ,IN

Keywords:

Craniofacial Fibrous Dysplasia, Maxilla, Monostotic, Polyostotic

Abstract

Introduction: Fibrous Dysplasia (FD) is a fibro-osseous lesion of the osseous structures of the body. The exact etiology is not known. Monostotic (when one bone is involved), polyostotic (when multiple bones are involved) and craniofacial are the three subtypes of craniofacial dysplasia. When the lesions are limited to contiguous bones of the craniofacial skeleton, it is termed as craniofacial dysplasia. McCune Albright syndrome is the triad of polyostotic fibrous dysplasia, Cafe aulait spots and endocrine pathology. Case Report: This case describes craniofacial dysplasia in a 30 year old female patient who had unusual presentation on the right side of the face involving maxilla, sphenoid, ethmoid and orbit. The clinical features, radiological findings and treatment have been discussed.

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Published

2021-01-01

Issue

Volume 8, Issue 1, January-June 2021

Section

Original Article

 

References

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