Papillon - Lefevre Syndrome: A Case Report of Two Siblings


Affiliations

  • Sri Aurobindo College of Dentistry, Department of Periodontology and Principal, Indore, India

Abstract

Papillon- Lefevre Syndrome (PLS) is an autosomal recessive disorder characterized by severe periodontitis and palmoplantar hyperkeratosis. Microbial lipopolysaccharides and mutations of cathepsin C gene has been suggested as the most probable etiological factors for PLS. This article presents a case of a thirteen year old female and her sibling suffering from the disease.

Keywords

Papillon- Lefevre Syndrome, Palmoplantar Hyperkeratosis, Early Onset Periodontitis

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