Embryonal Rhabdomyosarcoma as a Gingival Growth: A Rare Presentation


Affiliations

  • Government Dental College and Hospital, Asarwa, Department of Oral Medicine and Radiology, Ahemedabad, Gujarat, 380016, India
  • Government Dental College and Hospital, Asarwa, Department of Oral Medicine and Radiology, Ahmedabad, Gujarat, 380016, India

Abstract

Rhabdomyosarcoma (RMS) is a malignant tumor of striated muscle composed of neoplastic mesenchymal cells with varying degrees of cell differentiation. It accounts 60% of all soft-tissue sarcomas in children and only 2-5% in adults. Typical pediatric rhabdomyosarcoma variants like embryonal and alveolar sub-types are less frequently occur in adults. It has predilection for viscera followed by the head and neck region. RMS occurs in the head and neck region with 35% and 10-12% in the oral cavity. Establishment of the correct diagnosis and histological sub-type is of very importance in the treatment of this disease, because of the rarity of this neoplasm in the adult population the treatment is not uniform in the literature. Here we present case of embryonal rhabdomyosarcoma as a gingival growth in a 26-year-old female with clinical, radiological, histo-pathological and immunohistochemical aspects.


Keywords

Embryonal, Rhabdomyosarcoma, Sarcomas

Subject Discipline

Dentistry

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